Pulmonary hypertension (PH) is a complex, progressing and debilitating disease associated
with poor prognosis. Chronic thromboembolic pulmonary hypertension (CTEPH) — a distinct
subtype of PH is the result of persisting pulmonary artery obstruction, most often
caused by single or multiple episodes of pulmonary embolism (PE) and it is defined
as elevated mean pulmonary arterial pressure (mPAP) ≥ 25 mm Hg that persists more than six months after diagnosis of PE despite appropriate anticoagulation
therapy [
[1]
].Keywords
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Article info
Publication history
Published online: February 04, 2016
Accepted:
January 20,
2016
Received:
January 11,
2016
Identification
Copyright
© 2016 European Federation of Internal Medicine. Published by Elsevier B.V. All rights reserved.