Letter to the Editor| Volume 32, e23-e24, July 2016

First data from Latvian chronic thromboembolic pulmonary hypertension registry

Published:February 04, 2016DOI:
      Pulmonary hypertension (PH) is a complex, progressing and debilitating disease associated with poor prognosis. Chronic thromboembolic pulmonary hypertension (CTEPH) — a distinct subtype of PH is the result of persisting pulmonary artery obstruction, most often caused by single or multiple episodes of pulmonary embolism (PE) and it is defined as elevated mean pulmonary arterial pressure (mPAP) ≥ 25 mm Hg that persists more than six months after diagnosis of PE despite appropriate anticoagulation therapy [
      • Piazza G.
      • Goldhaber S.Z.
      Chronic thromboembolic pulmonary hypertension.


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